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KMID : 0438520100170010116
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Journal of the Korean Society of Neonatology
2010 Volume.17 No. 1 p.116 ~ p.122
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A Case of Intestinal Hemangioma Complicated with Thrombocytopenia (Kasabach-Merritt syndrome) in Premature Infant
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Lee Young-Jin
Choi Soo-Jin-Na
Kim Yoon-Ha
Choi Young-Youn
Bae Sul-Hee
Song Eun-Song
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Abstract
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Kasabach-Merritt syndrome is a rare thrombocytopenic consumptive coagulopathy associated with a giant hemangioma. We experienced a case of unexplained ascites with thrombocytopenia in a 32 week premature infant. An exploratory laparotomy was performed to determine the cause of the refractory ascites and thrombocytopenia. An intestinal hemangioma was found, but, surgical removal was not performed due to the extensive involvement. Hemangioma was confirmed by SPECT (single-photon emission computed tomography) and the thrombocytopenia was treated with steroid therapy. It is recommended that hemangioma of the visceral organs should be suspected when unexplained thrombocytopenia and disseminated intravascular coagulopathy persist.
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KEYWORD
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Kasabach-Merritt syndrome, Thrombocytopenia, Intestinal hemangioma, Disseminated intravascular coagulopathy
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